East Sussex - Better Together
NHS

3.5.1 Cystic Fibrosis

Cystic Fibrosis (CF) services are delivered in Paediatric Cystic Fibrosis Centres and Adult Cystic Fibrosis Centres and may include outreach services at local hospitals.

GPs are responsible for prescribing:

  • long-term nutritional supplementation via gastrostomy or nasogastric tube feeding
  • all other chronic specific medication, for example long-term oral antibiotics, pancreatic enzyme replacement therapy and vitamin supplements

GPs are NOT responsible for prescribing:

  • mucolytics (such as dornase alfa and mannitol), for new patients
  • nebulised/inhaled antibiotics for new patients
  • IV antibiotics

Primary Care

Please contact the CCG Medicines Management Team for advice prior to prescribing any specialised medicines
E-mail: EHSCCG.medicinesqueries@nhs.net
Medicines Management Helpline: 01424 735633

Secondary Care

Please contact the ESHT Pharmacy department for advice prior to prescribing any specialised medicines 
E-mail: esh-tr.medicinesinformation@nhs.net
Medicines Information Helpline: 01323 413785

 

Related NICE guidance:

TA 266 (Nov 2012) Mannitol dry powder for inhalation for treating cystic fibrosis
TA 276 (Mar 2013) Colistimethate sodium and tobramycin dry powder inhalers for pseudomonal lung infection in cystic fibrosis
TA 398 (Jul 2016) Lumacaftor–ivacaftor for treating cystic fibrosis homozygous for the F508del mutation
NG78 (Oct 2017) Cystic fibrosis: diagnosis and management

  • First Line Drugs
  • Second Line Drugs
  • Specialist Initiated Drugs
  • Specialist Only Drugs
  • Mixed Status